HSMN
Incidental findings
+ve signs Distal wasting lower limb, pes cavus, absent ankle jerkers, plantars, foot drop, distal sensory loss
Differential diagnosis HSMN (Friedreich’s ataxia also causes pes cavus)
Function
Minimal disability
Extensions

  • Examine gait - steppage
  • Feel for lateral popliteal nerve thickening
  • Look for small muscle wasting hands
Notes

  • Both AR and Admodes of inheritance.
  • Type I = demyelinating, absent reflexes; II = axonal, normal reflexes